Budd-Chiari syndrome is a congestive hepatopathy caused by blockage of hepatic veins which also causes raised portal venous pressure which may lead to portal hypertension, ascites, etc.
occurs in 1/100,000 of the general population worldwide
75% of cases are due to thrombosis of the hepatic vein and these are regarded as being “Primary BCS”
25% are caused by external compression of the hepatic vein “Secondary BCS”
this is different to the related condition of veno-occlusive disease which can occur in bone marrow transplant recipients as a complication of their medications, and also with certain herbs